Romiplostim in children with chronic immune thrombocytopenia (ITP): the French experience

Br J Haematol. 2014 Jan;164(2):266-71. doi: 10.1111/bjh.12609. Epub 2013 Oct 24.

Abstract

A minority of children with chronic immune thrombocytopenia (ITP) require therapeutic intervention to prevent haemorrhagic risk. This retrospective national study evaluated romiplostim in childhood non-responsive or refractory chronic ITP. Between 2009 and 2012, 10 patients whose Buchanan score was 3-4 were treated with romiplostim. The median duration of thrombocytopenia was 1·9 years (0·8-15). The median duration of romiplostim treatment was 9 months (3-36). A response was observed in 5/10 patients (one complete, four partial). No serious adverse effect was noticed. The long-term benefit/risk balance of this innovative treatment is currently recorded by Centre de Référence National des Cytopénies Auto-immunes de l'Enfant.

Keywords: child; refractory immune thrombocytopenia; romiplostim.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • Female
  • Follow-Up Studies
  • France
  • Humans
  • Infant
  • Male
  • Purpura, Thrombocytopenic, Idiopathic / drug therapy*
  • Receptors, Fc / administration & dosage
  • Receptors, Fc / therapeutic use*
  • Recombinant Fusion Proteins / administration & dosage
  • Recombinant Fusion Proteins / adverse effects
  • Recombinant Fusion Proteins / therapeutic use*
  • Retrospective Studies
  • Thrombopoietin / administration & dosage
  • Thrombopoietin / adverse effects
  • Thrombopoietin / therapeutic use*
  • Treatment Outcome

Substances

  • Receptors, Fc
  • Recombinant Fusion Proteins
  • Thrombopoietin
  • romiplostim