Abstract
Background:
Sneddon-Wilkinson disease (SWD) is a rare chronic neutrophilic dermatosis. The first-line treatment is dapsone but resistance to treatment may sometimes pose a challenge.
Case report:
We report a multidrug-resistant patient who responded dramatically before gradually losing response to infliximab and then etanercept. Complete remission was again obtained with adalimumab.
Discussion:
Our case confirms the previously reported dramatic efficacy of anti-TNF biological agents in recalcitrant SWD but highlights the possibility of subsequent loss of response. Furthermore, it illustrates the efficacy of adalimumab in this indication.
Keywords:
Adalimumab; Anti-TNF; Biothérapie anti-TNFalpha; Dermatose neutrophilique; Maladie de Sneddon-Wilkinson; Neutrophilic dermatosis; Sneddon-Wilkinson disease.
Copyright © 2013 Elsevier Masson SAS. All rights reserved.
Publication types
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Case Reports
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English Abstract
MeSH terms
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Adalimumab
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Aged
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Anti-Inflammatory Agents / pharmacology
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Anti-Inflammatory Agents / therapeutic use*
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Antibodies, Monoclonal / pharmacology
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Antibodies, Monoclonal / therapeutic use*
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Antibodies, Monoclonal, Humanized / pharmacology
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Antibodies, Monoclonal, Humanized / therapeutic use*
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Drug Administration Schedule
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Drug Resistance
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Drug Substitution
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Etanercept
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Humans
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Immunoglobulin A / blood
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Immunoglobulin G / pharmacology
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Immunoglobulin G / therapeutic use*
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Immunosuppressive Agents / pharmacology
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Immunosuppressive Agents / therapeutic use
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Infliximab
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Male
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Monoclonal Gammopathy of Undetermined Significance / complications
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Neutrophil Infiltration
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PUVA Therapy
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Receptors, Tumor Necrosis Factor / therapeutic use*
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Skin Diseases, Vesiculobullous / complications
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Skin Diseases, Vesiculobullous / drug therapy*
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Skin Diseases, Vesiculobullous / immunology
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Skin Diseases, Vesiculobullous / pathology
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Tumor Necrosis Factor-alpha / antagonists & inhibitors*
Substances
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Anti-Inflammatory Agents
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Antibodies, Monoclonal
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Antibodies, Monoclonal, Humanized
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Immunoglobulin A
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Immunoglobulin G
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Immunosuppressive Agents
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Receptors, Tumor Necrosis Factor
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Tumor Necrosis Factor-alpha
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Infliximab
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Adalimumab
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Etanercept