Aortic root replacement in a patient with left ventricular noncompaction

Ann Thorac Surg. 2014 Jan;97(1):e1-3. doi: 10.1016/j.athoracsur.2013.08.017.

Abstract

We describe the case of a 57-year-old woman with noncompaction of the left ventricle and regurgitant bicuspid aortic valve who presented with progressive congestive heart failure and was successfully treated with aortic root replacement. The long-term outcome for these patients is poor because of progressive left ventricular impairment, increased rates of life-threatening arrhythmias, and intraventricular thrombi. To our knowledge, only 3 patient with noncompaction of the left ventricle has been reported to have undergone aortic valve replacement for severely regurgitant bicuspid aortic valve. Herein, we describe a patient with noncompaction of the left ventricle who underwent successful mechanical aortic root replacement.

Keywords: 18; 35.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aortic Valve / abnormalities*
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / surgery
  • Aortic Valve Insufficiency / complications
  • Aortic Valve Insufficiency / diagnostic imaging
  • Aortic Valve Insufficiency / surgery*
  • Bicuspid Aortic Valve Disease
  • Bioprosthesis
  • Cardiopulmonary Bypass / methods
  • Disease Progression
  • Echocardiography / methods
  • Female
  • Follow-Up Studies
  • Heart Failure / etiology
  • Heart Failure / physiopathology
  • Heart Failure / surgery
  • Heart Valve Diseases / diagnostic imaging
  • Heart Valve Diseases / surgery*
  • Heart Valve Prosthesis Implantation / methods*
  • Humans
  • Isolated Noncompaction of the Ventricular Myocardium / complications
  • Isolated Noncompaction of the Ventricular Myocardium / diagnostic imaging
  • Isolated Noncompaction of the Ventricular Myocardium / surgery*
  • Middle Aged
  • Rare Diseases
  • Risk Assessment
  • Treatment Outcome