FADD and caspase-8 mediate priming and activation of the canonical and noncanonical Nlrp3 inflammasomes

J Immunol. 2014 Feb 15;192(4):1835-46. doi: 10.4049/jimmunol.1302839. Epub 2014 Jan 22.

Abstract

The Nlrp3 inflammasome is critical for host immunity, but the mechanisms controlling its activation are enigmatic. In this study, we show that loss of FADD or caspase-8 in a RIP3-deficient background, but not RIP3 deficiency alone, hampered transcriptional priming and posttranslational activation of the canonical and noncanonical Nlrp3 inflammasome. Deletion of caspase-8 in the presence or absence of RIP3 inhibited caspase-1 and caspase-11 activation by Nlrp3 stimuli but not the Nlrc4 inflammasome. In addition, FADD deletion prevented caspase-8 maturation, positioning FADD upstream of caspase-8. Consequently, FADD- and caspase-8-deficient mice had impaired IL-1β production when challenged with LPS or infected with the enteropathogen Citrobacter rodentium. Thus, our results reveal FADD and caspase-8 as apical mediators of canonical and noncanonical Nlrp3 inflammasome priming and activation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis Regulatory Proteins / metabolism
  • Calcium-Binding Proteins / metabolism
  • Carrier Proteins / immunology*
  • Caspase 1 / metabolism
  • Caspase 8 / genetics
  • Caspase 8 / immunology
  • Caspase 8 / metabolism*
  • Caspases / metabolism
  • Caspases, Initiator
  • Citrobacter rodentium / immunology
  • Enterobacteriaceae Infections / immunology
  • Enzyme Activation
  • Fas-Associated Death Domain Protein / genetics
  • Fas-Associated Death Domain Protein / metabolism*
  • Inflammasomes / immunology*
  • Interleukin-1beta / metabolism
  • Lipopolysaccharides
  • Macrophages / immunology
  • Mice
  • Mice, Knockout
  • NLR Family, Pyrin Domain-Containing 3 Protein
  • Receptor-Interacting Protein Serine-Threonine Kinases / deficiency
  • Receptor-Interacting Protein Serine-Threonine Kinases / genetics
  • Transcription, Genetic

Substances

  • Apoptosis Regulatory Proteins
  • Calcium-Binding Proteins
  • Carrier Proteins
  • Fadd protein, mouse
  • Fas-Associated Death Domain Protein
  • Inflammasomes
  • Interleukin-1beta
  • Ipaf protein, mouse
  • Lipopolysaccharides
  • NLR Family, Pyrin Domain-Containing 3 Protein
  • Nlrp3 protein, mouse
  • Receptor-Interacting Protein Serine-Threonine Kinases
  • Ripk3 protein, mouse
  • Casp4 protein, mouse
  • Caspase 8
  • Caspases
  • Caspases, Initiator
  • Caspase 1