Reduced acetylcholine-induced channel activity in dystrophic mouse myotubes

J Neurol Sci. 1988 Mar;84(1):77-86. doi: 10.1016/0022-510x(88)90176-1.

Abstract

Single channel recording patch-clamp technique was used in the mouse to compare the acetylcholine (ACh)-induced channel behaviour between normal and dystrophic myotubes. While open time and slope conductance were equivalent, ACh-induced channel opening frequency was more than 4-fold reduced in dystrophic compared to normal myotubes. In addition, the steady-state phosphorylation of the ACh receptor (AChR), tested by immunoprecipitation of 32P-labeled cells, indicated that the alpha-subunit was more heavily phosphorylated in the dystrophic myotubes. We propose that the degree of alpha-subunit phosphorylation of the AChR, which parallels the reduced AChR-channel opening probability, determines desensitization of the AChR in dystrophic myotubes.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acetylcholine / pharmacology
  • Animals
  • Cell Line
  • Ion Channels / drug effects
  • Ion Channels / metabolism*
  • Ion Channels / physiology
  • Membrane Potentials / drug effects
  • Mice
  • Muscles / cytology
  • Muscles / metabolism
  • Muscles / physiology*
  • Muscular Dystrophy, Animal / metabolism
  • Muscular Dystrophy, Animal / physiopathology*
  • Phosphorylation
  • Receptors, Cholinergic / metabolism*
  • Receptors, Cholinergic / physiology

Substances

  • Ion Channels
  • Receptors, Cholinergic
  • Acetylcholine