Cytogenetic follow-up of chromosomal mosaicism detected in first-trimester prenatal diagnosis

Prenat Diagn. 2014 Aug;34(8):739-47. doi: 10.1002/pd.4358. Epub 2014 Apr 8.

Abstract

Objective: To contribute to the risk assessment of true fetal mosaicism after detection of a mosaic chromosomal anomaly in chorionic villus samples (CVS) in order to enable more effective counseling and pregnancy management.

Methods: We retrospectively reviewed 7112 consecutive CVS analyzed on both direct preparations and cultured cells. In 135 out of the 177 cases of mosaicism, we performed cytogenetic follow-up and determined the frequency of confined placental mosaicism (CPM) and true fetal mosaicism according to type and distribution of the cytogenetic abnormality.

Results: True fetal mosaicism was detected in 38 out of 135 cases (28.15%), confirming the higher incidence of CPM (71.85%). Confirmation rate of CV mosaicism depends on the combination of placental cell lineages affected, chromosome involved and mosaic versus non-mosaic chromosomal anomaly. The overall probability of fetal involvement significantly rises with involvement of mesenchymal cells: 5.88% abnormal cytotrophoblast, 20.96% abnormal mesenchyme and 58.97% anomalies in both tissues.

Conclusion: Most of the mosaic findings at CVS are unreliable indicators of the fetal karyotype. Our study contributes to large series with cytogenetic information from the different tissues along the cytotrophoblast-extraembrional mesoderm-fetus axis in order to infer clinical relevance of the findings and to enable more effective genetic counseling.

MeSH terms

  • Chorionic Villi Sampling*
  • Cytogenetic Analysis*
  • Female
  • Humans
  • Mosaicism*
  • Polyploidy
  • Pregnancy
  • Pregnancy Trimester, First
  • Retrospective Studies
  • Risk Assessment
  • Sex Chromosome Aberrations
  • Trisomy