Granulocyte-macrophage colony-stimulating factor reactivates fetal hemoglobin synthesis in erythroblast clones from normal adults

Blood. 1989 Dec;74(8):2657-67.

Abstract

Reactivation of fetal hemoglobin (HbF, alpha 2 gamma 2) synthesis was previously reported in normal human adult erythroblast colonies ("bursts") generated by erythroid progenitors (BFU-E) in fetal calf serum-supplemented (FCS+) semisolid cultures stimulated with erythropoietin (Ep). Our studies focused on the reactivation of HbF synthesis in normal adult erythroid bursts generated by peripheral blood mononuclear cells (PBMCs) seeded in FCS+ methylcellulose culture. Reactivation is almost totally suppressed when (a) PBMCs are grown in optimized FCS- culture, or (b) PBMCs are first stringently depleted of monocytes and then plated in FCS+ medium (ie, BFU-E growth in FCS+ Mo- culture). In both experimental conditions, the proliferation of lymphocytes and macrophages interspersed among colonies is drastically reduced, and the cloning efficiency of granulocyte-macrophage (GM) progenitors is sharply diminished. In either case, addition of biosynthetic GM colony-stimulating factor (GM-CSF) induces a dose-related increase of HbF synthesis up to the level in FCS+ culture, with even more elevated values on delayed addition of Ep. A dose-related increase was also observed in erythroblast clones generated by highly purified BFU-E. These results suggest that reactivation of HbF synthesis in normal adults is at least in part mediated by GM-CSF. Furthermore, they imply intriguing hypotheses on the mechanism(s) of perinatal Hb switching. Finally, they raise the possibility of reactivation of HbF synthesis in beta-thalassemia and sickle cell anemia by GM-CSF therapy.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Biological Factors / pharmacology
  • Cells, Cultured
  • Colony-Stimulating Factors / pharmacology*
  • Culture Media
  • Cytokines
  • Dose-Response Relationship, Drug
  • Erythroblasts / metabolism*
  • Erythropoiesis / drug effects*
  • Erythropoietin / pharmacology
  • Fetal Hemoglobin / biosynthesis*
  • Globins / biosynthesis
  • Granulocyte-Macrophage Colony-Stimulating Factor
  • Growth Substances / pharmacology*
  • Humans
  • In Vitro Techniques
  • Isoelectric Point

Substances

  • Biological Factors
  • Colony-Stimulating Factors
  • Culture Media
  • Cytokines
  • Growth Substances
  • Erythropoietin
  • Granulocyte-Macrophage Colony-Stimulating Factor
  • Globins
  • Fetal Hemoglobin