Successful percutaneous management of Lutembacher syndrome

Indian Heart J. 2014 May-Jun;66(3):355-7. doi: 10.1016/j.ihj.2014.03.016. Epub 2014 May 15.

Abstract

Background: The surgical management of Lutembacher syndrome is straight forward but percutaneous management, though technically demanding, is always desirable.

Methods: A 17 year old unmarried female presented with severe Mitral stenosis and a 19 mm almost circular Ostium secundum ASD with moderate pulmonary artery hypertension and dilated right sided chambers. She was managed in a staged manner. Percutaneous trans mitral commissurotomy (PTMC) was done first, using a 26 mm Inoue balloon catheter set, and after 48 h, ASD was closed with a 20 mm Cocoon Septal Occluder.

Results: The mitral valve area increased after PTMC from 0.8 cm2 to 2.1 cm2 and QP/QS decreased from 4.9 to 2. ASD was successfully closed under echocardiographic and fluoroscopic guidance.

Conclusion: Percutaneous management of the Lutembacher syndrome (PTMC and ASD device closure) is an effective and low risk procedure and avoids considerable morbidity and mental trauma for the patients.

Keywords: Lutembacher syndrome; Mitral stenosis; Ostium secundum; PTMC.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Cardiac Catheterization / instrumentation*
  • Cardiac Surgical Procedures / instrumentation*
  • Echocardiography
  • Female
  • Fluoroscopy
  • Humans
  • Lutembacher Syndrome / diagnostic imaging
  • Lutembacher Syndrome / surgery*
  • Septal Occluder Device*
  • Surgery, Computer-Assisted