The article is devoted to the use of minimally invasive techniques for removing intraventricular tumors; this topic is currently relevant to pediatric neurosurgery. As an example, a clinical case of complete removal of a choroid plexus papilloma in a child using the neuroendoscopic technique through the biportal approach is provided. This tumor is most commonly found in pediatric practice. Taking this into account, the use of minimally invasive surgical methods for treating this pathology is very important. The published data relating to this pathology, as well as to the use of neuroendoscopy for this disease, are fragmentary today. Therefore, one of the objectives of this work was to analyze the literature regarding etiopathogenesis, clinical presentation, diagnostic features, and some aspects of surgical treatment of choroid plexus papilloma, in connection with which this work is primarily of practical interest.