Resolution of airflow obstruction on polysomnography after laryngotracheal reconstruction with anterior tracheal wall suspension in a patient with DiGeorge Syndrome

Int J Pediatr Otorhinolaryngol. 2014 Oct;78(10):1799-803. doi: 10.1016/j.ijporl.2014.07.035. Epub 2014 Aug 2.

Abstract

DiGeorge Syndrome (DGS) may be associated with airway abnormalities including laryngomalacia and suprastomal collapse of the trachea (SCT), which may lead to sleep disordered breathing (SDB). We present a 4-year-old boy with DGS, SCT, and SDB by polysomnography (PSG) while the tracheostomy tube was capped. The patient underwent anterior tracheal wall suspension (ATWS) with concurrent tracheostomy decannulation. Following the repair, the patient experienced improved airway patency visually and by PSG with resolution of obstructive sleep apnea and hypoventilation. ATWS is an effective method to repair SCT in selected patients and may lead to early decannulation and improvement of SDB.

Keywords: Anterior cricoid suspension; Anterior tracheal wall suspension; DiGeorge Syndrome; Obstructive sleep apnea; Sleep disordered breathing.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Device Removal
  • DiGeorge Syndrome / complications*
  • DiGeorge Syndrome / surgery
  • Humans
  • Male
  • Plastic Surgery Procedures / methods*
  • Polysomnography
  • Sleep Apnea Syndromes / etiology*
  • Sleep Apnea Syndromes / surgery
  • Trachea / surgery*
  • Tracheostomy