Treatment of congenital pulmonary lymphangiectasia using ethiodized oil lymphangiography

J Perinatol. 2014 Sep;34(9):720-2. doi: 10.1038/jp.2014.71.

Abstract

Historically, congenital pulmonary lymphangiectasia (CPL) has had poor treatment outcomes despite aggressive therapy. There are recent reports of ethiodized oil (Lipiodol) lymphangiography successfully treating lymphatic leakage in adults. In this report, we describe two infants with CPL complicated by chylothoraces successfully treated by instillation of ethiodized oil into the lymphatic system. Congenital atresia of the thoracic duct was demonstrated on the lymphangiogram in both patients before treatment. Both patients have shown good short-term outcomes without supplemental oxygen or fat restricted diets at 9 months of age. Ethiodized oil lymphangiography represents a new treatment modality for some patients with CPL.

Publication types

  • Case Reports

MeSH terms

  • Contrast Media / therapeutic use*
  • Embolization, Therapeutic
  • Ethiodized Oil / therapeutic use*
  • Female
  • Humans
  • Infant
  • Lung Diseases / congenital*
  • Lung Diseases / diagnostic imaging
  • Lung Diseases / drug therapy
  • Lymphangiectasis / congenital*
  • Lymphangiectasis / diagnostic imaging
  • Lymphangiectasis / drug therapy
  • Lymphography*

Substances

  • Contrast Media
  • Ethiodized Oil

Supplementary concepts

  • Lymphangiectasia, pulmonary, congenital