Association of clinicopathological characteristics with secondary neoplastic lymphoproliferative disorders in patients with lymphomatoid papulosis

Leuk Lymphoma. 2015 May;56(5):1303-7. doi: 10.3109/10428194.2014.958821. Epub 2014 Nov 5.

Abstract

Lymphomatoid papulosis (LyP) refers to an indolent cutaneous lymphoma. The association of prognostic clinicopathological risk factors with a second hematologic malignancy has not yet been determined. We investigated the prognostic effect of clinicopathological characteristics on the occurrence of a second lymphoma, as well as the first-line treatment, in 24 patients diagnosed with LyP using logistic regression models. We showed that lymphoma occurrence was associated with a lower mean age at onset of LyP symptoms, histological types B and C, head-located LyP lesions and a higher frequency of LyP recurrences. In multivariate analyses, histologic type A was associated with a lower risk of second lymphoma (odds ratio [OR] = 0.12, 95% confidence interval [CI] 0.014-0.98; p = 0.045) adjusting for age of LyP first symptomatology, and an important increased lymphoma-free survival rate (long-rank test; p = 0.06). Clinicopathological characteristics are important in defining the clearance or persistence of LyP lesions and may predict the occurrence of a second lymphoma.

Keywords: Lymphoma and Hodgkin disease; chemotherapeutic approaches; prognostication.

MeSH terms

  • Adult
  • Aged
  • Female
  • Follow-Up Studies
  • Humans
  • Kaplan-Meier Estimate
  • Lymphomatoid Papulosis / diagnosis*
  • Lymphomatoid Papulosis / genetics
  • Lymphomatoid Papulosis / mortality
  • Lymphomatoid Papulosis / therapy
  • Lymphoproliferative Disorders / diagnosis*
  • Lymphoproliferative Disorders / mortality
  • Male
  • Middle Aged
  • Neoplasms, Second Primary*
  • Odds Ratio
  • Recurrence
  • Skin Neoplasms / diagnosis*
  • Skin Neoplasms / genetics
  • Skin Neoplasms / mortality
  • Skin Neoplasms / therapy
  • Time Factors
  • Young Adult