ALCAPA and massive pulmonary atelectasis: how a stent in the airway can be life-saving

Paola Serio; Enrico Chiappa; Valentina Fainardi; Silvia Favilli; Bruno Murzi; Roberto Baggi; Luigi Arcieri; Roberto Leone; Lorenzo Mirabile

doi:10.1016/j.ijporl.2014.08.044

ALCAPA and massive pulmonary atelectasis: how a stent in the airway can be life-saving

Int J Pediatr Otorhinolaryngol. 2014 Nov;78(11):2015-7. doi: 10.1016/j.ijporl.2014.08.044. Epub 2014 Sep 6.

Authors

Paola Serio¹, Enrico Chiappa², Valentina Fainardi³, Silvia Favilli², Bruno Murzi⁴, Roberto Baggi⁵, Luigi Arcieri⁴, Roberto Leone⁶, Lorenzo Mirabile⁵

Affiliations

¹ Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy. Electronic address: [email protected].
² Pediatric Cardiology Unit, Meyer Children Hospital, Florence, Italy.
³ Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy; Department of Paediatrics, Parma Children Hospital, Parma, Italy.
⁴ Pediatric Cardiac Surgery, Heart Hospital, G. Monasterio Tuscany Foundation, Massa, Italy.
⁵ Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy.
⁶ Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy; Department of Anesthesia and Intensive Care, Ospedale Riuniti di Foggia, Foggia, Italy.

PMID: 25245256
DOI: 10.1016/j.ijporl.2014.08.044

Abstract

Anomalous left coronary artery from pulmonary artery (ALCAPA) is a rare congenital anomaly in which left coronary artery arises from the pulmonary artery resulting in progressive myocardial ischemia and dysfunction of the left ventricle. We report a case of ALCAPA with severe cardiac and respiratory failure and huge heart dilation compressing the left main bronchus and preventing from an effective ventilation. Emergency bronchial stenting allowed to improve left lung atelectasis, reduce pulmonary hypertension, resume anterograde left coronary artery perfusion and stabilize cardiovascular conditions to undertake a successful surgical correction.

Keywords: Airway stent; Alcapa syndrome; Atelectasis; Cardiac arrest; Respiratory distress; Stent.

Publication types

Case Reports

MeSH terms

Bland White Garland Syndrome / complications*
Bronchi
Female
Heart Failure / etiology
Heart Failure / therapy*
Humans
Hypertension, Pulmonary / etiology
Hypertension, Pulmonary / therapy
Infant
Pulmonary Atelectasis / etiology
Pulmonary Atelectasis / therapy*
Respiratory Insufficiency / etiology
Respiratory Insufficiency / therapy*
Stents*