Interstrain differences in the progression of nonalcoholic steatohepatitis to fibrosis in mice are associated with altered hepatic iron metabolism

J Nutr Biochem. 2014 Dec;25(12):1235-42. doi: 10.1016/j.jnutbio.2014.06.012. Epub 2014 Aug 19.

Abstract

Nonalcoholic fatty liver disease (NAFLD) is a major health problem worldwide. Currently, there is a lack of conclusive information to clarify the molecular events and mechanisms responsible for the progression of NAFLD to fibrosis and cirrhosis and, more importantly, for differences in interindividual disease severity. The aim of this study was to investigate a role of interindividual differences in iron metabolism among inbred mouse strains in the pathogenesis and severity of fibrosis in a model of NAFLD. Feeding male A/J, 129S1/SvImJ and WSB/EiJ mice a choline- and folate-deficient diet caused NAFLD-associated liver injury and iron metabolism abnormalities, especially in WSB/EiJ mice. NAFLD-associated fibrogenesis was correlated with a marked strain- and injury-dependent increase in the expression of iron metabolism genes, especially transferrin receptor (Tfrc), ferritin heavy chain (Fth1), and solute carrier family 40 (iron-regulated transporter), member 1 (Slc40a1, Fpn1) and their related proteins, and pronounced down-regulation of the iron regulatory protein 1 (IRP1), with the magnitude being A/J<129S1/SvImJ<WSB/EiJ. Mechanistically, down-regulation of IRP1 was linked to an increased expression of microRNAs miR-200a and miR-223, which was negatively correlated with IRP1. The results of this study demonstrate that the interstrain variability in the extent of fibrogenesis was associated with a strain-dependent deregulation of hepatic iron homeostasis.

Keywords: IRP1; Iron metabolism; Liver fibrogenesis; Methyl-deficient diet; NAFLD; miR-200a.

MeSH terms

  • Animals
  • Apoferritins / genetics
  • Apoferritins / metabolism
  • Cation Transport Proteins / genetics
  • Cation Transport Proteins / metabolism
  • Choline Deficiency / complications
  • Choline Deficiency / pathology
  • Disease Progression
  • Down-Regulation
  • Ferroportin
  • Folic Acid Deficiency / complications
  • Folic Acid Deficiency / pathology
  • Hepatocytes / cytology
  • Hepatocytes / metabolism
  • Iron / metabolism*
  • Iron Regulatory Protein 1 / genetics
  • Iron Regulatory Protein 1 / metabolism
  • Liver / metabolism*
  • Liver / pathology
  • Liver Cirrhosis / pathology*
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Inbred Strains
  • MicroRNAs / genetics
  • MicroRNAs / metabolism
  • Non-alcoholic Fatty Liver Disease / pathology*
  • Receptors, Transferrin / genetics
  • Receptors, Transferrin / metabolism

Substances

  • Cation Transport Proteins
  • MIRN223 microRNA, mouse
  • MicroRNAs
  • Mirn200 microRNA, mouse
  • Receptors, Transferrin
  • Tfrc protein, mouse
  • Ferroportin
  • Apoferritins
  • Iron
  • Iron Regulatory Protein 1