Sporadic giant mesenteric fibromatosis

Indian J Surg Oncol. 2014 Sep;5(3):242-5. doi: 10.1007/s13193-014-0342-3. Epub 2014 Aug 2.

Abstract

Mesenteric fibromatosis is an uncommon tumour which is locally aggressive without any metastatic potential and can occur as a sporadic event or in association with familial adenomatous polyposis syndrome. Giant mesenteric fibromatosis is very rare and is a diagnostic and therapeutic challenge. This is a case report of a rare presentation of deep fibromatosis as a sporadic giant intrabdominal mesenteric tumour in a 29 year old male managed by surgical excision and definitive diagnosis made on the basis of immunohistochemical findings.

Keywords: Desmoid tumors; Familial adenomatous polyposis; Mesenteric fibromatosis.