Numerical and structural chromosomal anomalies in undifferentiated pleomorphic sarcoma

Anticancer Res. 2014 Dec;34(12):7119-27.

Abstract

Background: Malignant fibrous histiocytoma (MFH) or undifferentiated pleomorphic sarcoma (UPS) is the most common soft-tissue sarcoma of late adult life. Further advances in genetic characterization are warranted. The aim of this study was to search for numerical and structural chromosomal anomalies in UPS.

Materials and methods: We investigated five sarcoma-specific chromosomal translocations, five oncogene amplifications as well as the numerical karyotype of 19 UPS samples and one UPS/MFH cell line (U2197) using FISH probes on interphase nuclei.

Results: Our results demonstrate that chromosomal translocations involving CHOP, SYT, EWS, FUS and FKHR genes are absent. Furthermore, amplification of ERBB2 (10.5%) and MDM2 (10.5%) was observed whereas the EGFR, C-MYC and N-MYC genes were not amplified. Interestingly, predominant aneuploidies were found in eight chromosomes.

Conclusion: The data demonstrate rarity of sarcoma-specific chromosomal breaks and oncogene amplifications in UPS, yet polysomic chromosomes appear more characteristically in this condition.

Keywords: Chromosome aberrations; aneuploidy; fluorescent in situ hybridization; gene amplification; sarcoma.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Cell Line, Tumor
  • Chromosome Breakage*
  • ErbB Receptors / biosynthesis
  • ErbB Receptors / genetics
  • Female
  • Forkhead Box Protein O1
  • Forkhead Transcription Factors / genetics
  • Gene Amplification / genetics*
  • Histiocytoma, Malignant Fibrous / genetics*
  • Humans
  • Karyotyping
  • Male
  • Middle Aged
  • Proto-Oncogene Proteins / genetics
  • Proto-Oncogene Proteins c-mdm2 / biosynthesis
  • Proto-Oncogene Proteins c-mdm2 / genetics
  • Proto-Oncogene Proteins c-myc / biosynthesis
  • Proto-Oncogene Proteins c-myc / genetics
  • RNA-Binding Protein EWS / genetics
  • RNA-Binding Protein FUS / genetics
  • Receptor, ErbB-2 / biosynthesis
  • Receptor, ErbB-2 / genetics
  • Repressor Proteins / genetics
  • Transcription Factor CHOP / genetics
  • Translocation, Genetic / genetics*

Substances

  • DDIT3 protein, human
  • FOXO1 protein, human
  • Forkhead Box Protein O1
  • Forkhead Transcription Factors
  • MYC protein, human
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-myc
  • RNA-Binding Protein EWS
  • RNA-Binding Protein FUS
  • Repressor Proteins
  • SS18 protein, human
  • Transcription Factor CHOP
  • MDM2 protein, human
  • Proto-Oncogene Proteins c-mdm2
  • EGFR protein, human
  • ERBB2 protein, human
  • ErbB Receptors
  • Receptor, ErbB-2