Association of N-acetylcysteine and glucagon during percutaneous cholangiography in the treatment of inspissated bile syndrome

Arch Pediatr. 2015 Mar;22(3):300-2. doi: 10.1016/j.arcped.2014.12.007. Epub 2015 Jan 19.

Abstract

Inspissated bile syndrome (IBS) is a rare neonatal disease. In the majority of cases, it resolves spontaneously and treatment is conservative. Follow-up is recommended with close monitoring of laboratory tests. When IBS does not resolve spontaneously, a catheter can be inserted into the gallbladder for cholangiography, which allows irrigation and drainage. Despite this treatment, some biliary tract obstruction may persist. We report on the case of a 3-month-old infant whose continuous biliary obstruction caused by IBS was successfully managed by interventional radiology with the association of N-acetylcysteine and glucagon. Even as first-line agents, these would allow more rapid clearance of gallstones and prevent infectious complications of indwelling catheters as well as decrease the need for surgery.

Publication types

  • Case Reports

MeSH terms

  • Acetylcysteine / therapeutic use*
  • Bile
  • Child, Preschool
  • Cholangiography / methods
  • Cholestasis, Extrahepatic / diagnostic imaging
  • Cholestasis, Extrahepatic / drug therapy*
  • Cholestasis, Extrahepatic / etiology
  • Drug Therapy, Combination
  • Female
  • Glucagon / therapeutic use*
  • Humans
  • Syndrome

Substances

  • Glucagon
  • Acetylcysteine