Kawasaki disease (KD) is a systemic vasculitis which presents with stable vital signs. Shock rarely occurs in such cases, but it may occur in the acute phase of KD. This report describes a 7-year-old boy with KD shock syndrome (KDSS) who presented with persistent fever, injected conjunctiva, a polymorphic skin rash, echocardiography indicating coronary artery dilatation, and shock. The patient's haemodynamic status markedly improved with immunoglobulin therapy. Early recognition of KDSS can be challenging; however, delay in diagnosis can increase the risk of coronary artery abnormalities and death.
Keywords: Immunoglobulin; Kawasaki disease; Shock.