Invasive desmoplastic fibroblastoma in the chest wall

Ann Thorac Surg. 2015 Apr;99(4):e85-6. doi: 10.1016/j.athoracsur.2015.01.055.

Abstract

Desmoplastic fibroblastoma is a rare soft tissue tumor. We present the case of a 61-year-old man with a growing chest wall tumor in the pleural cavity. After resection, the tumor was diagnosed as desmoplastic fibroblastoma. This is the first report of desmoplastic fibroblastoma occurring in the chest wall. Generally, desmoplastic fibroblastoma is considered as a benign and slow-growing tumor. However, the tumor in our patient grew very rapidly and invaded the adjacent lung, parietal pleura, and periosteum of the rib bone. We therefore describe this tumor as an "invasive" desmoplastic fibroblastoma.

Publication types

  • Case Reports

MeSH terms

  • Biopsy, Needle
  • Bone Neoplasms / diagnosis
  • Bone Neoplasms / pathology*
  • Bone Neoplasms / surgery*
  • Fibroma, Desmoplastic / diagnosis
  • Fibroma, Desmoplastic / pathology*
  • Fibroma, Desmoplastic / surgery*
  • Follow-Up Studies
  • Humans
  • Immunohistochemistry
  • Male
  • Middle Aged
  • Neoplasm Invasiveness / pathology
  • Neoplasm Staging
  • Positron-Emission Tomography / methods
  • Rare Diseases
  • Soft Tissue Neoplasms / diagnosis
  • Soft Tissue Neoplasms / pathology*
  • Soft Tissue Neoplasms / surgery*
  • Thoracic Wall / pathology*
  • Thoracic Wall / surgery
  • Time Factors
  • Tomography, X-Ray Computed / methods
  • Treatment Outcome