Familial late-onset Alzheimer's disease: description of an Italian family with four affected siblings and one case of early-onset dementia in the preceding generation

Aging Clin Exp Res. 2016 Oct;28(5):991-5. doi: 10.1007/s40520-015-0383-7. Epub 2015 May 27.

Abstract

We describe a family composed of six siblings, four of which affected by late-onset Alzheimer's disease (LOAD). We constructed the family pedigree, evaluated mutations usually associated with early-onset Alzheimer's disease (APP, PSEN1, PSEN2), and assessed polymorphisms in the apolipoprotein E (APOE) gene and in cytokine genes that we had previously found to be associated with a higher risk of LOAD (IL-10, IL-6, TNF-α). Results showed that all subjects carried one ε4 allele of the APOE gene and those with the earliest age of onset exhibited the AA (-1082) IL-10 and the CC (-174) IL-6 genotypes. The only male had a genetic profile which also included the A (-308) TNF-α allele. These data confirm the role of the APOE gene as genetic risk factor in LOAD, and suggest that the risk of developing AD may be governed by a "susceptibility profile" involving polymorphisms in inflammatory genes.

Keywords: Apolipoprotein E; Cytokines; Familial Alzheimer’s disease; Genetic susceptibility; Inflammation; Late-onset Alzheimer’s disease.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aged, 80 and over
  • Alleles
  • Alzheimer Disease / genetics*
  • Dementia / genetics*
  • Female
  • Genotype
  • Humans
  • Italy
  • Male
  • Polymorphism, Genetic
  • Siblings*