Multiple and aggressive pulmonary vein transcatheter interventions as bridge to transplantation in primary diffuse pulmonary vein stenosis

Catheter Cardiovasc Interv. 2015 Oct;86(4):E190-3. doi: 10.1002/ccd.25920. Epub 2015 May 27.

Abstract

Primary diffuse congenital pulmonary vein stenosis (PDPVS) is a severe condition with poor prognosis. No therapeutic strategy has been found to be effective in its management to date. We report the case of a premature child with severe PDPVS who underwent multiple transcatheter interventions as bridge to heart-lung transplantation.

Keywords: cardiac catheterization/intervention; heart-lung; pediatric; pulmonary arteries/veins; pulmonary vascular resistance/hypertension; transplantation.

MeSH terms

  • Cardiac Catheterization / methods*
  • Cardiac Catheterization / statistics & numerical data
  • Constriction, Pathologic / diagnostic imaging
  • Constriction, Pathologic / therapy
  • Follow-Up Studies
  • Heart-Lung Transplantation
  • Humans
  • Hypertension, Pulmonary / diagnosis
  • Hypertension, Pulmonary / therapy
  • Infant
  • Infant, Premature*
  • Pulmonary Circulation / physiology*
  • Pulmonary Veins / abnormalities
  • Pulmonary Veins / diagnostic imaging
  • Pulmonary Veno-Occlusive Disease / diagnostic imaging*
  • Pulmonary Veno-Occlusive Disease / therapy*
  • Radiography
  • Risk Assessment
  • Time Factors