Unexpected functions of nuclear factor-κB during germinal center B-cell development: implications for lymphomagenesis

Curr Opin Hematol. 2015 Jul;22(4):379-87. doi: 10.1097/MOH.0000000000000160.

Abstract

Purpose of review: B-cell tumors originating from the transformation of germinal center B cells frequently harbor genetic mutations, leading to constitutive activation of the nuclear factor-κB (NF-κB) signaling pathway. The present review highlights recent insights into the roles of separate NF-κB transcription factors in germinal center B-cell development and discusses implications of the results for germinal center lymphomagenesis.

Recent findings: Understanding how aberrant NF-κB activation promotes tumorigenesis requires the understanding of the role of NF-κB in the tumor-precursor cells. Despite extensive knowledge on NF-κB biology, the function of this complex signaling pathway in the differentiation of germinal center B cells is largely unknown. The present review will discuss recent findings that revealed distinct roles of separate NF-κB transcription factors during the germinal center reaction in the context of germinal center lymphomagenesis. Most notably, a single NF-κB subunit, c-REL, was found to be required for the maintenance of the germinal center reaction and was associated with the activation of a metabolic program that promotes cell growth.

Summary: Identifying the biological roles of the separate NF-κB transcription factor subunits in germinal center biology will help to better understand the pathogenic consequences of their constitutive activation in B-cell tumors. This knowledge may be exploited for the development of targeted antitumor therapies aimed at inhibiting selectively those components of aberrant NF-κB activity which contribute to pathogenesis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • B-Lymphocytes / metabolism
  • B-Lymphocytes / pathology
  • Carcinogenesis / genetics
  • Carcinogenesis / metabolism*
  • Carcinogenesis / pathology
  • Cell Differentiation
  • Gene Expression Regulation, Neoplastic*
  • Germinal Center / metabolism
  • Germinal Center / pathology
  • Humans
  • Lymphoma / genetics
  • Lymphoma / metabolism*
  • Lymphoma / pathology
  • NF-kappa B / genetics*
  • NF-kappa B / metabolism
  • Neoplastic Stem Cells / metabolism
  • Neoplastic Stem Cells / pathology
  • Protein Subunits / genetics*
  • Protein Subunits / metabolism
  • Signal Transduction

Substances

  • NF-kappa B
  • Protein Subunits