Hypoplastic Left Heart Syndrome With Right Ventricle Compression

Tai Fuchigami; Masahiko Nishioka; Kazuhiro Takahashi; Toru Akashige; Nobuhiro Nagata

doi:10.1016/j.athoracsur.2015.04.100

Hypoplastic Left Heart Syndrome With Right Ventricle Compression

Ann Thorac Surg. 2015 Jul;100(1):e15-7. doi: 10.1016/j.athoracsur.2015.04.100.

Authors

Tai Fuchigami¹, Masahiko Nishioka², Kazuhiro Takahashi³, Toru Akashige², Nobuhiro Nagata²

Affiliations

¹ Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan. Electronic address: [email protected].
² Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.
³ Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.

PMID: 26140801
DOI: 10.1016/j.athoracsur.2015.04.100

Abstract

A male neonate presented with the aortic atresia-mitral stenosis (AA-MS) variant of hypoplastic left heart syndrome (HLHS) wherein the suprasystemic left ventricular (LV) pressure and large left ventricle shifted the intraventricular septum. A compressed right ventricle made it difficult to maintain stroke volume. To avoid high right ventricular (RV) volume load and output, we used a 2-stage Norwood-Glenn (NW-G) procedure. Bilateral pulmonary artery banding (bPAB) was performed on day of life (DOL) 4. On DOL 58, we performed percutaneous balloon dilation of the bPAB portion. At age 3 months, the NW-G procedure was performed without peripheral pulmonary hypoplasia. The patient is currently doing well.

Publication types

Case Reports

MeSH terms

Cardiac Surgical Procedures
Heart Diseases / etiology
Heart Diseases / surgery
Heart Ventricles*
Humans
Hypoplastic Left Heart Syndrome / complications*
Hypoplastic Left Heart Syndrome / surgery
Infant, Newborn
Male
Pressure