We evaluated the incidence and outcome of lung involvement in 35 patients with autoimmune pancreatitis (AIP). Our results indicate that lung involvement is commonly observed in AIP (40%). In addition, corticosteroid treatment improved the lung lesions and appeared to reduce the probability of relapse compared with pancreatic lesions (0% vs 36%). This is the first report to assess the long-term outcome of lung involvement in AIP (52 ± 33 months).
Keywords: autoimmune pancreatitis; immunoglobulin G4; immunoglobulin G4-related disease; immunoglobulin G4-related lung disease; type 1 autoimmune pancreatitis.
© 2015 Asian Pacific Society of Respirology.