Rare Presentation of Supratentorial Primitive Neuroectodermal Tumors Mimicking Bifocal Germ Cell Tumors: 2 Case Reports

J Pediatr Hematol Oncol. 2016 Mar;38(2):e67-70. doi: 10.1097/MPH.0000000000000402.

Abstract

Bifocal pineal and suprasellar tumors have only been described in the context of germ cell tumors in the pediatric age group. We report 2 patients with radiologic findings of bifocal pineal and suprasellar lesions, with a histologic diagnosis of supratentorial primitive neuroectodermal tumor. The absence of diabetes insipidus and other endocrine abnormalities was noteworthy in both cases. This observation challenges previous reports on the pathognomonic value of this clinico-radiologic entity.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Child, Preschool
  • Female
  • Humans
  • Male
  • Neoplasms, Germ Cell and Embryonal / pathology
  • Neoplasms, Multiple Primary / pathology*
  • Neuroectodermal Tumors, Primitive / pathology*
  • Pineal Gland / pathology
  • Supratentorial Neoplasms / pathology*