Drug reaction with eosinophilia and systemic symptoms (DRESS): clinicopathological study of 45 cases

J Eur Acad Dermatol Venereol. 2015 Nov;29(11):2199-205. doi: 10.1111/jdv.13212. Epub 2015 Sep 9.

Abstract

Background: Drug reaction with eosinophilia and systemic symptoms (DRESS) is a rare and severe adverse drug reaction. Large detailed studies of histopathological features of DRESS are sparse and suggest an association between keratinocyte damage and the severity of visceral involvement.

Objectives: To describe the dermatopathological features in a large series of DRESS and their possible association with clinical features and the severity of the disease.

Methods: A retrospective analysis of the clinicobiological and dermatopathological features in a monocentric cohort of patients with DRESS.

Results: From January 2005 to January 2013, 45 patients were validated as probable or definite cases of DRESS. The median age was 64 years (range 3-87). The most frequent clinical and biological features included: fever ≥38.5°C (95%), facial oedema (72%), enlarged lymph nodes (51%), visceral involvement (75%), blood eosinophilia (97%) and atypical lymphocytes (82%). Severe DRESS occurred in 24% and a fatal outcome in 6% of patients. Histopathological analysis showed that no specific histopathological pattern was characteristic for DRESS. However, several changes in different cutaneous compartments were observed in 2 of 3 of cases. Spongiosis (55%) and keratinocyte damage (53%) were the most common epidermal changes. Spongiosis was associated with non-severe DRESS (P = 0.041) whereas confluent keratinocyte necrosis correlated with severe DRESS (P = 0.011). Vascular changes were frequent (88%). A moderate dermal perivascular lymphocytic infiltrate was invariably present, containing eosinophils, neutrophils and/or atypical lymphocytes in 57% of cases.

Conclusions: Epidermal changes are indicative for the severity of DRESS.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Child
  • Child, Preschool
  • Drug Hypersensitivity Syndrome / complications
  • Drug Hypersensitivity Syndrome / pathology*
  • Edema / etiology*
  • Epidermis / pathology*
  • Face*
  • Female
  • Fever / etiology
  • Humans
  • Keratinocytes / pathology*
  • Lymphatic Diseases / etiology
  • Lymphocytes / pathology
  • Male
  • Middle Aged
  • Necrosis
  • Retrospective Studies
  • Severity of Illness Index
  • Young Adult