Congenital atresia of the left main coronary artery in an adult: A rare anomaly with an unfavorable prognosis. Review of the literature

Cardiovasc Revasc Med. 2015 Dec;16(8):498-502. doi: 10.1016/j.carrev.2015.08.006. Epub 2015 Aug 21.

Abstract

Congenital atresia of the left main coronary artery (LMCA) is one of the rarest congenital anomalies, which may have an unfavorable prognosis leading to myocardial ischemia, ventricle dysfunction or even sudden cardiac death. There are 34 cases of LMCA in adults reported in the literature, most of them successfully treated with coronary revascularization. We report the case of an adult with LMCA who presented with terminal heart failure that required biventricular assistance and heart transplant.

Keywords: Coronary artery anomaly; Left main coronary artery atresia.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Age Factors
  • Aged
  • Cause of Death
  • Coronary Angiography / methods
  • Coronary Vessel Anomalies / diagnosis*
  • Coronary Vessel Anomalies / mortality*
  • Coronary Vessel Anomalies / surgery
  • Dyspnea / diagnosis
  • Dyspnea / etiology
  • Heart Failure / diagnosis
  • Heart Failure / etiology
  • Heart Failure / surgery*
  • Heart Transplantation / methods*
  • Humans
  • Imaging, Three-Dimensional*
  • Magnetic Resonance Imaging, Cine / methods
  • Male
  • Prognosis
  • Rare Diseases
  • Risk Assessment
  • Sex Factors
  • Survival Analysis
  • Treatment Outcome