Abstract
Rosai-Dorfman disease is a rare non-Langerhans cell histiocytosis, mainly involving cervical nodes. We present the case of a patient with a pulmonary form of Rosai-Dorfman disease without peripheral or intra-thoracic lymph nodes, characterized by the presence of pulmonary nodules and cysts associated with bilateral pleural effusions.
MeSH terms
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Adrenal Cortex Hormones / therapeutic use
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Aged
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Biopsy
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Cysts / diagnosis
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Cysts / drug therapy
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Cysts / etiology*
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Drug Therapy, Combination
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Histiocytosis, Sinus / complications*
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Histiocytosis, Sinus / diagnosis
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Histiocytosis, Sinus / drug therapy
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Humans
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Immunohistochemistry
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Immunosuppressive Agents / therapeutic use
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Male
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Multiple Pulmonary Nodules / diagnosis
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Multiple Pulmonary Nodules / drug therapy
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Multiple Pulmonary Nodules / etiology*
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Pleural Effusion / diagnosis
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Pleural Effusion / drug therapy
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Pleural Effusion / etiology*
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Predictive Value of Tests
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Tomography, X-Ray Computed
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Treatment Outcome
Substances
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Adrenal Cortex Hormones
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Immunosuppressive Agents