Translation and Assembly of Radiolabeled Mitochondrial DNA-Encoded Protein Subunits from Cultured Cells and Isolated Mitochondria

Methods Mol Biol. 2016:1351:115-29. doi: 10.1007/978-1-4939-3040-1_9.

Abstract

In higher eukaryotes, the mitochondrial electron transport chain consists of five multi-subunit membrane complexes responsible for the generation of cellular ATP. Of these, four complexes are under dual genetic control as they contain subunits encoded by both the mitochondrial and nuclear genomes, thereby adding another layer of complexity to the puzzle of respiratory complex biogenesis. These subunits must be synthesized and assembled in a coordinated manner in order to ensure correct biogenesis of different respiratory complexes. Here, we describe techniques to (1) specifically radiolabel proteins encoded by mtDNA to monitor the rate of synthesis using pulse labeling methods, and (2) analyze the stability, assembly, and turnover of subunits using pulse-chase methods in cultured cells and isolated mitochondria.

Keywords: Blue-native PAGE (BN-PAGE ); Complex assembly; Mitochondria; Mitochondrial DNA (mtDNA); Oxidative phosphorylation (OXPHOS ); Pulse labeling; Pulse-chase labeling; Respiratory chain.

MeSH terms

  • Animals
  • Brain / cytology
  • Cells, Cultured
  • DNA, Mitochondrial / genetics*
  • Electron Transport / physiology*
  • Electron Transport Chain Complex Proteins / analysis*
  • Electron Transport Chain Complex Proteins / genetics
  • Electrophoresis, Gel, Two-Dimensional / methods*
  • Liver / cytology
  • Mice
  • Mitochondria / genetics
  • Mitochondrial Membranes / metabolism
  • Mitochondrial Proteins / metabolism
  • Muscle, Skeletal / cytology
  • Myocardium / cytology
  • Oxidative Phosphorylation
  • Protein Biosynthesis / genetics*
  • Protein Subunits / genetics
  • Staining and Labeling / methods

Substances

  • DNA, Mitochondrial
  • Electron Transport Chain Complex Proteins
  • Mitochondrial Proteins
  • Protein Subunits