Mode of delivery and risk of intracranial haemorrhage in newborns with severe haemophilia A: a multicentre study in Gulf region

Haemophilia. 2016 May;22(3):e134-8. doi: 10.1111/hae.12842. Epub 2015 Nov 11.

Abstract

Introduction: The optimum mode of delivery in a known carrier of a haemophilia A is still an issue of debate.

Aim: This study was conducted to report a multicentre experience in Gulf Cooperation Council (GCC) on the incidence of intracranial haemorrhage (ICH) in newborns with severe haemophilia A delivered by different modalities.

Methods: We have conducted a retrospective/prospective multicentre cohort study including a total of seven hospitals distributed in four GCC countries between 1998 and Jan 2015. A total of 163 patient with severe haemophilia A (factor VIII <1%) were enrolled in this study, age ranged between 2 weeks to 18 years.

Results: Most of the patients were born by spontaneous vaginal delivery (SVD) (131, 80.4%), whereas 26 patients (16%) were born by CS and only six patients were born by instrumental delivery (3.7%), five of them by vacuum and one was delivered using forceps. Five out of 163 patients developed ICH during the first 2 weeks of life (3.1%). Two of them were born by SVD (2/131; 1.5%) and two were born by instrumental delivery (2/6; 33.3%). Only one patient among those who were born by caesarean section developed ICH (1/26; 3.8%). Assisted vaginal delivery was associated with a significant risk of ICH, in comparison to SVD and CS (P = 0.0093).

Conclusion: Normal vaginal delivery is still considered a safe journey through the birth canal for haemophilic newborns particularly in this area of the world. Larger prospective studies might be needed to define an evidence-based optimal mode of delivery for the haemophilia carrier expecting an affected child.

Keywords: Gulf region; haemophilia A; intracranial haemorrhage; mode of delivery.

Publication types

  • Comparative Study
  • Multicenter Study

MeSH terms

  • Adolescent
  • Cesarean Section / statistics & numerical data*
  • Child
  • Child, Preschool
  • Cohort Studies
  • Delivery, Obstetric / statistics & numerical data*
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Intracranial Hemorrhages / epidemiology*
  • Male
  • Middle East / epidemiology
  • Pregnancy Complications, Hematologic / epidemiology*
  • Pregnancy*
  • Prospective Studies
  • Retrospective Studies
  • Risk