Rapid Deterioration of the Renal Function Caused by the Coexistence of Intratubular Amyloidosis and Myeloma Cast Nephropathy

Intern Med. 2015;54(23):3023-8. doi: 10.2169/internalmedicine.54.5174. Epub 2015 Dec 1.

Abstract

Multiple myeloma presents with various kidney injuries, including cast nephropathy, light chain deposition disease, and amyloidosis. Cast nephropathy is the most common form and mostly consists of monoclonal immunoglobulin light chains with Tamm-Horsfall protein. Immunoglobulin light chain (AL) amyloidosis may affect all compartments of the kidney, but it is rare in the tubuli. We herein present a rare case with rapid progression of renal failure caused by the co-occurrence of intratubular amyloidosis and cast nephropathy due to multiple myeloma. Our case suggests unique amyloidogenic light chain cast, which can form amyloid fibrils under specific tubular fluid conditions, and illustrates the complicated light chain pathophysiology.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Amyloid / metabolism
  • Amyloidosis / complications
  • Amyloidosis / diagnosis*
  • Amyloidosis / therapy
  • Antineoplastic Combined Chemotherapy Protocols
  • Creatinine / metabolism*
  • Humans
  • Immunoglobulin Light Chains / metabolism*
  • Immunoglobulin Light-chain Amyloidosis
  • Kidney Diseases / diagnosis*
  • Kidney Diseases / etiology
  • Kidney Diseases / therapy
  • Male
  • Paraproteinemias / complications
  • Renal Dialysis
  • Renal Insufficiency / diagnosis*
  • Renal Insufficiency / etiology
  • Renal Insufficiency / therapy
  • Treatment Outcome

Substances

  • Amyloid
  • Immunoglobulin Light Chains
  • Creatinine