Abstract
We present a rare late manifestation of systemic venous collaterals in a 17-year-old female, 16 years after bidirectional cavopulmonary anastomosis, resulting in clinically unacceptable desaturation with progressive effort intolerance and cyanosis.
Keywords:
after bidirectional cavopulmonary anastomosis; double-outlet right ventricle; giant azygous vein.
MeSH terms
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Adolescent
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Azygos Vein / abnormalities*
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Azygos Vein / diagnostic imaging*
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Collateral Circulation
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Cyanosis / diagnostic imaging*
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Echocardiography
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Female
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Fontan Procedure / adverse effects*
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Heart Defects, Congenital / diagnostic imaging*
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Heart Defects, Congenital / surgery
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Humans
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Pulmonary Artery / surgery
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Radiography
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Tomography, X-Ray Computed
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Vena Cava, Superior / surgery