Introduction: Best's disease is a progressive macular dystrophy, beginning either in childhood or adolescence.
Case study: We report a rare case of choroidal neovascularization complicating vitelliform dystrophy in a child of 8 years with bilateral progressive loss of visual acuity. The ophthalmoscopic examination showed vitelliform lesions in both foveas. Fluorescein angiography confirmed a subretinal neovascular membrane in the left eye. Additional testing also confirmed the diagnosis of Best's disease associated with choroidal neovascularization.
Discussion: Best's vitelliform macular dystrophy is often asymptomatic because visual acuity tends to remain stable for a long time. A sudden loss of vision suggests the occurrence of complications, such as choroidal neovascularization.
Keywords: Angiographie à la fluorescéine; Best's disease; Choroidal neovascularization; Dystrophie vitelliforme; Fluorescein angiography; Macula; Maladie de Best; Néovascularisation choroïdienne; Vitelliform dystrophy.
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