Kikuchi-Fujimoto Disease Associated With Subcutaneous Panniculitis-Like T-Cell Lymphoma

Am J Dermatopathol. 2016 Jun;38(6):e77-80. doi: 10.1097/DAD.0000000000000486.

Abstract

Subcutaneous panniculitis-like T-cell lymphoma (SPTL) is a variant of cutaneous T-cell lymphoma that can mimic inflammatory panniculitis, particularly lupus erythematosus panniculitis, clinically and histologically. Patients with SPTL generally have a benign course, though SPTL can be complicated by hemophagocytic syndrome, which can negatively impact prognosis. We report a patient with recurrent SPTL and hemophagocytic syndrome accompanied by a necrotizing lymphadenitis consistent with Kikuchi-Fujimoto disease. SPTL and Kikuchi-Fujimoto disease have not previously been reported to occur together, but share many overlapping features. The relationship between these disorders, LE-associated panniculitis, and lupus lymphadenitis deserves further exploration.

MeSH terms

  • Histiocytic Necrotizing Lymphadenitis / complications*
  • Histiocytic Necrotizing Lymphadenitis / pathology
  • Humans
  • Immunohistochemistry
  • Immunophenotyping
  • Lymphohistiocytosis, Hemophagocytic / complications
  • Lymphohistiocytosis, Hemophagocytic / pathology
  • Lymphoma, T-Cell / complications*
  • Lymphoma, T-Cell / pathology
  • Male
  • Panniculitis / complications*
  • Panniculitis / pathology
  • Young Adult

Supplementary concepts

  • Subcutaneous panniculitis-like T-cell lymphoma