Age- and brain region-dependent α-synuclein oligomerization is attributed to alterations in intrinsic enzymes regulating α-synuclein phosphorylation in aging monkey brains

Oncotarget. 2016 Feb 23;7(8):8466-80. doi: 10.18632/oncotarget.6445.

Abstract

We previously reported that the levels of α-syn oligomers, which play pivotal pathogenic roles in age-related Parkinson's disease (PD) and dementia with Lewy bodies, increase heterogeneously in the aging brain. Here, we show that exogenous α-syn incubated with brain extracts from older cynomolgus monkeys and in Lewy body pathology (LBP)-susceptible brain regions (striatum and hippocampus) forms higher amounts of phosphorylated and oligomeric α-syn than that in extracts from younger monkeys and LBP-insusceptible brain regions (cerebellum and occipital cortex). The increased α-syn phosphorylation and oligomerization in the brain extracts from older monkeys and in LBP-susceptible brain regions were associated with higher levels of polo-like kinase 2 (PLK2), an enzyme promoting α-syn phosphorylation, and lower activity of protein phosphatase 2A (PP2A), an enzyme inhibiting α-syn phosphorylation, in these brain extracts. Further, the extent of the age- and brain-dependent increase in α-syn phosphorylation and oligomerization was reduced by inhibition of PLK2 and activation of PP2A. Inversely, phosphorylated α-syn oligomers reduced the activity of PP2A and showed potent cytotoxicity. In addition, the activity of GCase and the levels of ceramide, a product of GCase shown to activate PP2A, were lower in brain extracts from older monkeys and in LBP-susceptible brain regions. Our results suggest a role for altered intrinsic metabolic enzymes in age- and brain region-dependent α-syn oligomerization in aging brains.

Keywords: Gerotarget; aging; brain; polo-like kinase 2; protein phosphatase 2A; α-synuclein.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aging / physiology*
  • Animals
  • Apoptosis
  • Blotting, Western
  • Brain / metabolism*
  • Cell Proliferation
  • Ceramides / metabolism
  • Corpus Striatum / metabolism
  • Glucosylceramidase / metabolism*
  • Hippocampus / metabolism
  • Lewy Bodies / metabolism
  • Lewy Bodies / pathology
  • Macaca fascicularis
  • Phosphorylation
  • Protein Multimerization
  • Protein Phosphatase 2 / metabolism*
  • Protein Serine-Threonine Kinases / metabolism*
  • alpha-Synuclein / chemistry*
  • alpha-Synuclein / metabolism*

Substances

  • Ceramides
  • alpha-Synuclein
  • Protein Serine-Threonine Kinases
  • Protein Phosphatase 2
  • Glucosylceramidase