Juvenile otosclerosis: a case presentation and review of the literature

BMJ Case Rep. 2016 Apr 15:2016:10.1136/bcr-2015-214232. doi: 10.1136/bcr-2015-214232.

Abstract

Otosclerosis in childhood and adolescence or juvenile otosclerosis is a rare disorder resulting in conductive hearing loss. A 9-year-old boy presented to our clinic, suffering from moderate hearing loss. According to his parents, his hearing acuity had progressively deteriorated over the past 2 years. Otoscopy and tympanometry revealed bilateral secretory otitis media and the patient underwent bilateral grommet insertion. However, he continued to report of hearing loss and a right exploratory tympanotomy was performed. Stapedial fixation was confirmed, being compatible with juvenile otosclerosis, and we proceeded to a right stapedotomy. One year later, follow-up showed satisfactory outcome with an air-bone gap closure to 10 dB. Juvenile otosclerosis with the coexistence of persistent secretory otitis media can be overlooked. Affected children from 9 years of age are strongly motivated to undergo stapes surgery for juvenile otosclerosis, following parental consent.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Child
  • Hearing Loss, Conductive / etiology*
  • Humans
  • Male
  • Otitis Media with Effusion / complications
  • Otosclerosis / complications*
  • Otosclerosis / surgery
  • Stapes Surgery / methods