This review highlights the data currently available on the activity of systemic therapy in chondrosarcoma, chordoma, giant cell tumour of the bone (GCTB) and solitary fibrous tumour, i.e., four rare sarcomas amongst mesenchymal malignancy arising from the skull base.
Keywords: Chondrosarcoma; Chordoma; Giant cell tumour; Sarcoma; Skull base; Solitary fibrous tumour.