Differentiation of benign and malignant hilar bile duct stenosis

J Surg Res. 2016 Jun 15;203(2):275-82. doi: 10.1016/j.jss.2016.03.002. Epub 2016 Mar 25.

Abstract

Background: Failure to differentiate benign and malignant hilar bile duct stenosis may lead to inappropriate treatment. We retrospectively analyzed the methods for differentiation.

Materials and methods: A total of 53 patients with hilar bile duct stenosis were included, comprising 41 malignant cases (hilar cholangiocarcinoma) and 12 benign cases (six primary sclerosing cholangitis and six IgG4-associated sclerosing cholangitis). Data of clinical histories, laboratory tests, imaging studies, and liver pathologies were collected, and comparison was made between benign and malignant groups.

Results: Compared with malignant group, patients in the benign group were more likely to have multiorgan involvement of clinical histories (P < 0.001). There was no difference on bilirubin, liver enzyme, and serum tumor marker between the two groups, whereas serum IgG4 levels were higher in the benign group (P = 0.003). Patients in the benign group were more likely to have pancreatic changes (P < 0.001) and multiple-segmental bile duct stenosis (P < 0.001) on imaging. Compared with the malignant group, patients in the benign group were more likely to show severe periportal inflammation in noninvolved liver (P < 0.001), fibrosis around intrahepatic bile duct (P < 0.001), and more IgG4-positive plasma cells (P < 0.001) on liver pathology.

Conclusions: Benign lesion should be considered for patients with history of multiorgan involvement, pancreas changes, or multiple-segmental bile duct stenosis on imaging. Liver biopsy could be helpful for differential diagnosis before surgery.

Keywords: Benign; Biliary stenosis; Hilar cholangiocarcinoma; Sclerosing cholangitis.

MeSH terms

  • Adult
  • Aged
  • Bile Duct Neoplasms / complications
  • Bile Duct Neoplasms / diagnosis*
  • Bile Ducts, Extrahepatic*
  • Cholangitis, Sclerosing / complications
  • Cholangitis, Sclerosing / diagnosis*
  • Cholestasis, Extrahepatic / etiology*
  • Diagnosis, Differential
  • Female
  • Humans
  • Klatskin Tumor / complications
  • Klatskin Tumor / diagnosis*
  • Male
  • Middle Aged
  • Retrospective Studies
  • Risk Factors