Frequency and Clinical Characteristics of Intrachromosomal Amplification of Chromosome 21 in Korean Childhood B-lineage Acute Lymphoblastic Leukemia

Ann Lab Med. 2016 Sep;36(5):475-80. doi: 10.3343/alm.2016.36.5.475.

Abstract

Background: Intrachromosomal amplification of chromosome 21 (iAMP21) is known to be associated with poor prognosis in B-cell ALL (B-ALL). To determine the frequency and clinical characteristics of iAMP21 in Korean B-ALL patients, we performed FISH and multiplex ligation-dependent probe amplification (MLPA) analyses.

Methods: A total of 102 childhood B-ALL patients were screened with ETV6-RUNX1 FISH probes (Abbott Molecular, USA). The presence of an iAMP21 was confirmed by using MLPA P327 iAMP21-ERG probemix (MRC Holland, The Netherlands).

Results: iAMP21 was detected in one of the screened B-ALL patients (1/102 patients, 1.0%) who presented the ALL immunophenotype and complex karyotype at initial diagnosis. The patient relapsed twice after bone marrow transplantation. MLPA showed 12.5-Mb and 4.28-Mb regions of amplification and deletion, respectively.

Conclusions: The frequency of iAMP21 is considerable in Korean pediatric patients. Our report suggests that iAMP21 in childhood B-ALL has very unfavorable impact on patient's prognosis. Additional methods such as MLPA analysis is essential to rule out patients with equivocal interphase FISH results.

Keywords: Acute lymphoblastic leukemia; Childhood; ERG; FISH; Korean; MLPA; RUNX1; iAMP21.

MeSH terms

  • Adolescent
  • Asian People / genetics*
  • B-Lymphocytes / metabolism*
  • Child
  • Child, Preschool
  • Chromosomes, Human, Pair 21*
  • Core Binding Factor Alpha 2 Subunit / genetics
  • DNA Probes / metabolism
  • ETS Translocation Variant 6 Protein
  • Female
  • Humans
  • Immunophenotyping
  • In Situ Hybridization, Fluorescence
  • Infant
  • Infant, Newborn
  • Male
  • Multiplex Polymerase Chain Reaction
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / diagnosis*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / genetics
  • Proto-Oncogene Proteins c-ets / genetics
  • Repressor Proteins / genetics
  • Republic of Korea
  • Translocation, Genetic
  • Young Adult

Substances

  • Core Binding Factor Alpha 2 Subunit
  • DNA Probes
  • Proto-Oncogene Proteins c-ets
  • RUNX1 protein, human
  • Repressor Proteins