An inflammatory and trophic disconnect biomarker profile revealed in Down syndrome plasma: Relation to cognitive decline and longitudinal evaluation

Alzheimers Dement. 2016 Nov;12(11):1132-1148. doi: 10.1016/j.jalz.2016.05.001. Epub 2016 Jul 21.

Abstract

Introduction: Given that Alzheimer's pathology develops silently over decades in Down syndrome (DS), prognostic biomarkers of dementia are a major need.

Methods: We investigated the plasma levels of Aβ, proNGF, tPA, neuroserpin, metallo-proteases and inflammatory molecules in 31 individuals with DS (with and without dementia) and in 31 healthy controls. We examined associations between biomarkers and cognitive decline.

Results: Aβ40 and Aβ42 were elevated in DS plasma compared to controls, even in DS individuals without dementia. Plasma Aβ correlated with the rate of cognitive decline across 2 years. ProNGF, MMP-1, MMP-3, MMP-9 activity, TNF-α, IL-6, and IL-10 were higher in DS plasma, even at AD-asymptomatic stages. Declining plasma Aβ42 and increasing proNGF levels correlated with cognitive decline. A combined measure of Aβ and inflammatory molecules was a strong predictor of prospective cognitive deterioration.

Conclusions: Our findings support the combination of plasma and cognitive assessments for the identification of DS individuals at risk of dementia.

Keywords: Alzheimer's disease; Amyloid-β; Biomarker; Blood; Down syndrome; Inflammation; MMP-3; MMP-9; Metallo-proteases; Nerve growth factor; Plasma; proNGF.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Amyloid beta-Peptides / blood
  • Biomarkers / blood
  • Cognitive Dysfunction / blood
  • Cognitive Dysfunction / etiology
  • Cognitive Dysfunction / immunology
  • Cytokines / blood
  • Disease Progression
  • Down Syndrome / blood*
  • Down Syndrome / immunology*
  • Down Syndrome / psychology
  • Female
  • Humans
  • Longitudinal Studies
  • Male
  • Matrix Metalloproteinase 3 / blood
  • Matrix Metalloproteinase 9 / blood
  • Middle Aged
  • Nerve Growth Factor / blood
  • Neuropeptides / blood
  • Neuroserpin
  • Peptide Fragments / blood
  • Prospective Studies
  • Protein Precursors / blood
  • Serpins / blood
  • Tissue Plasminogen Activator / blood
  • Young Adult

Substances

  • Amyloid beta-Peptides
  • Biomarkers
  • Cytokines
  • Neuropeptides
  • Peptide Fragments
  • Protein Precursors
  • Serpins
  • amyloid beta-protein (1-40)
  • amyloid beta-protein (1-42)
  • pro-nerve growth factor, human
  • Nerve Growth Factor
  • Tissue Plasminogen Activator
  • MMP3 protein, human
  • Matrix Metalloproteinase 3
  • MMP9 protein, human
  • Matrix Metalloproteinase 9

Grants and funding