Characterization of prion protein function by focal neurite stimulation

J Cell Sci. 2016 Oct 15;129(20):3878-3891. doi: 10.1242/jcs.183137. Epub 2016 Sep 2.

Abstract

The cellular prion protein (PrPC), encoded by the PRNP gene, is a ubiquitous glycoprotein, which is highly expressed in the brain. This protein, mainly known for its role in neurodegenerative diseases, is involved in several physiological processes including neurite outgrowth. By using a novel focal stimulation technique, we explored the potential function of PrPC, in its soluble form, as a signaling molecule. Thus, soluble recombinant prion proteins (recPrP) encapsulated in micro-vesicles were released by photolysis near the hippocampal growth cones. Local stimulation of wild-type growth cones with full-length recPrP induced neurite outgrowth and rapid growth cone turning towards the source. This effect was shown to be concentration dependent. Notably, PrPC-knockout growth cones were insensitive to recPrP stimulation, but this property was rescued in PrP-knockout growth cones expressing GFP-PrP. Taken together, our findings indicate that recPrP functions as a signaling molecule, and that its homophilic interaction with membrane-anchored PrPC might promote neurite outgrowth and facilitate growth cone guidance.

Keywords: Growth cone guidance and signaling; Local delivery; Neurite outgrowth; Prion protein.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antibodies, Monoclonal / pharmacology
  • Cell Membrane / drug effects
  • Cell Membrane / metabolism
  • Growth Cones / drug effects
  • Growth Cones / metabolism
  • Mice
  • Neural Cell Adhesion Molecules / metabolism
  • Neurites / drug effects
  • Neurites / metabolism*
  • Prion Proteins / metabolism*
  • Protein Binding / drug effects
  • Protein Kinase Inhibitors / pharmacology
  • Recombinant Proteins / metabolism
  • Signal Transduction / drug effects

Substances

  • Antibodies, Monoclonal
  • Neural Cell Adhesion Molecules
  • Prion Proteins
  • Protein Kinase Inhibitors
  • Recombinant Proteins