Allogeneic hematopoietic stem cell transplant in adult patients with myelodysplastic syndrome/myeloproliferative neoplasm (MDS/MPN) overlap syndromes

Leuk Lymphoma. 2017 Apr;58(4):872-881. doi: 10.1080/10428194.2016.1217529. Epub 2016 Aug 11.

Abstract

MDS/MPN (myelodysplastic syndrome/myeloproliferative neoplasm) overlap syndromes are myeloid malignancies for which allogeneic hematopoietic stem cell transplant (allo-HSCT) is potentially curative. We describe transplant outcomes of 43 patients - 35 with chronic myelomonocytic leukemia, CMML (of which 17 had blast transformation, BT) and eight with MDS/MPN-unclassifiable (MDS/MPN,U). At median follow-up of 21 months, overall survival (OS), cumulative incidence of relapse (CIR) and non-relapse mortality (NRM) were 55%, 29%, and 25% respectively in CMML without BT and 47%, 40%, and 34% respectively in CMML with BT. Higher HSCT-comorbidity index (HSCT-CI >3 versus ≤3; p = 0.015) and splenomegaly (p = 0.006) predicted worse OS in CMML without BT. In CMML with BT, engraftment failure (p = 0.006) and higher HSCT-CI (p = 0.03) were associated with inferior OS, while HSCT within 1-year of diagnosis was associated with improved OS (p = 0.045). In MDS/MPN,U, at median follow-up of 15 months, OS, CIR, and NRM were 62%, 30%, and 14%, respectively.

Keywords: MDS/MPN overlap syndrome; MDS/MPN-unclassifiable; allogeneic hematopoietic stem cell transplant; chronic myelomonocytic leukemia (CMML).

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Biomarkers
  • Female
  • Graft vs Host Disease / etiology
  • Hematopoietic Stem Cell Transplantation* / adverse effects
  • Hematopoietic Stem Cell Transplantation* / methods
  • Humans
  • Male
  • Middle Aged
  • Myelodysplastic Syndromes / diagnosis
  • Myelodysplastic Syndromes / mortality
  • Myelodysplastic Syndromes / therapy*
  • Myeloproliferative Disorders / diagnosis
  • Myeloproliferative Disorders / mortality
  • Myeloproliferative Disorders / therapy*
  • Phenotype
  • Prognosis
  • Recurrence
  • Survival Analysis
  • Syndrome
  • Transplantation Conditioning
  • Transplantation, Homologous
  • Young Adult

Substances

  • Biomarkers