Neuropsychiatric characteristics of GBA-associated Parkinson disease

J Neurol Sci. 2016 Nov 15:370:63-69. doi: 10.1016/j.jns.2016.08.059. Epub 2016 Aug 30.

Abstract

Mutations in GBA1 are a well-established risk factor for Parkinson disease (PD). GBA-associated PD (GBA-PD) may have a higher burden of nonmotor symptoms than idiopathic PD (IPD). We sought to characterize the relationship between GBA-PD and neuropsychiatric symptoms. Subjects were screened for common GBA1 mutations. GBA-PD (n=31) and non-carrier (IPD; n=55) scores were compared on the Unified Parkinson Disease Rating Scale (UPDRS), Montreal Cognitive Assessment (MoCA), Beck Depression Inventory (BDI), and the State-Trait Anxiety Index (STAI). In univariate comparisons, GBA-PD had a greater prevalence of depression (33.3%) versus IPD (13.2%) (p<0.05). In regression models controlling for age, sex, disease duration, motor disability, and MoCA score, GBA-PD had an increased odds of depression (OR 3.66, 95% CI 1.13-11.8) (p=0.03). Post-hoc analysis stratified by sex showed that, among men, GBA-PD had a higher burden of trait anxiety and depression than IPD; this finding was sustained in multivariate models. Among women, GBA-PD did not confer greater psychiatric morbidity than IPD. These results suggest that GBA1 mutations confer greater risk of neuropsychiatric morbidity in PD, and that sex may affect this association.

Keywords: Anxiety; Depression; GBA1; Glucocerebrosidase; Parkinson disease.

MeSH terms

  • Aged
  • Anxiety / complications
  • Anxiety / genetics*
  • Anxiety / physiopathology
  • Comorbidity
  • Depression / complications
  • Depression / genetics*
  • Depression / physiopathology
  • Disability Evaluation
  • Female
  • Genetic Association Studies
  • Genetic Predisposition to Disease
  • Glucosylceramidase
  • Heterozygote
  • Humans
  • Male
  • Middle Aged
  • Mutation*
  • Neuropsychological Tests
  • Parkinson Disease / complications
  • Parkinson Disease / genetics*
  • Parkinson Disease / physiopathology
  • Parkinson Disease / psychology*
  • Psychiatric Status Rating Scales
  • Severity of Illness Index
  • Sex Factors
  • Tertiary Care Centers
  • Time Factors
  • beta-Glucosidase / genetics*

Substances

  • beta-Glucosidase
  • GBA2 protein, human
  • Glucosylceramidase