Multifocal Congenital Hemangiopericytoma

Pediatr Dermatol. 2017 Jan;34(1):e69-e73. doi: 10.1111/pde.13031. Epub 2016 Nov 22.

Abstract

Congenital hemangiopericytoma (HPC) is a rare mesenchymal tumor with less aggressive behavior and a more favorable prognosis than similar tumors in adults. Multifocal presentation is even less common than isolated HPC and hence its clinical and histologic recognition may be challenging. A newborn infant with multifocal congenital HPC causing severe deformity but with a favorable outcome after chemotherapy and surgical removal is reported.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Biomarkers, Tumor / metabolism
  • Cyclophosphamide / therapeutic use
  • Dactinomycin / therapeutic use
  • Forearm
  • Hemangiopericytoma / diagnosis*
  • Hemangiopericytoma / drug therapy
  • Hemangiopericytoma / metabolism
  • Humans
  • Infant, Newborn
  • Magnetic Resonance Imaging
  • Male
  • Soft Tissue Neoplasms / diagnosis*
  • Soft Tissue Neoplasms / drug therapy
  • Soft Tissue Neoplasms / metabolism
  • Vincristine / therapeutic use

Substances

  • Biomarkers, Tumor
  • Dactinomycin
  • Vincristine
  • Cyclophosphamide

Supplementary concepts

  • VAC protocol