Experiences in microarray-based evaluation of developmental disabilities and congenital anomalies

Clin Genet. 2017 Oct;92(4):372-379. doi: 10.1111/cge.12978. Epub 2017 Mar 30.

Abstract

Background: Chromosomal microarray analysis is the first-tier test for the evaluation of developmental disabilities and congenital anomalies. In this report, we present CMA results of 971 patient and 301 parent samples.

Materials and methods: Among 971 patient samples, 133 (13.6%) had pathogenic variants.

Results: While analyzing, an "in-house" variant database was also used besides other databases. Owing to this, we have found chance to report the most frequent benign variants in Turkish population.

Conclusion: With the additional data we acquired in this study, we also emphasized the high potential of CMA in revealing single gene disorders and novel gene-phenotype associations as well as copy number variations.

Keywords: CNV; VOUS; ZNF107; Turkish; microarray; microdeletion; microduplication; optima; pathogenic.

MeSH terms

  • Chromosome Aberrations*
  • Congenital Abnormalities / genetics*
  • Congenital Abnormalities / pathology
  • DNA Copy Number Variations / genetics*
  • Developmental Disabilities / genetics*
  • Developmental Disabilities / pathology
  • Humans
  • Microarray Analysis
  • Turkey