RIPK3 Restricts Viral Pathogenesis via Cell Death-Independent Neuroinflammation

Cell. 2017 Apr 6;169(2):301-313.e11. doi: 10.1016/j.cell.2017.03.011. Epub 2017 Mar 30.

Abstract

Receptor-interacting protein kinase-3 (RIPK3) is an activator of necroptotic cell death, but recent work has implicated additional roles for RIPK3 in inflammatory signaling independent of cell death. However, while necroptosis has been shown to contribute to antiviral immunity, death-independent roles for RIPK3 in host defense have not been demonstrated. Using a mouse model of West Nile virus (WNV) encephalitis, we show that RIPK3 restricts WNV pathogenesis independently of cell death. Ripk3-/- mice exhibited enhanced mortality compared to wild-type (WT) controls, while mice lacking the necroptotic effector MLKL, or both MLKL and caspase-8, were unaffected. The enhanced susceptibility of Ripk3-/- mice arose from suppressed neuronal chemokine expression and decreased central nervous system (CNS) recruitment of T lymphocytes and inflammatory myeloid cells, while peripheral immunity remained intact. These data identify pleiotropic functions for RIPK3 in the restriction of viral pathogenesis and implicate RIPK3 as a key coordinator of immune responses within the CNS.

Keywords: RIPK1; RIPK3; West Nile virus; chemokines; necroptosis; neuroimmunology; neuroinflammation.

MeSH terms

  • Animals
  • Central Nervous System / metabolism
  • Chemokines / immunology
  • Leukocytes / immunology
  • Macrophages / immunology
  • Mice
  • Mice, Inbred C57BL
  • Necrosis
  • Neurons / metabolism
  • Receptor-Interacting Protein Serine-Threonine Kinases / metabolism*
  • West Nile Fever / immunology*
  • West Nile virus / physiology*

Substances

  • Chemokines
  • Receptor-Interacting Protein Serine-Threonine Kinases
  • Ripk1 protein, mouse
  • Ripk3 protein, mouse