Follow-up of Children with Kernicterus in Kano, Nigeria

J Trop Pediatr. 2018 Jun 1;64(3):176-182. doi: 10.1093/tropej/fmx041.

Abstract

Introduction: Acute bilirubin encephalopathy (ABE) is associated with long-term sequelae (kernicterus). It continues to be a significant issue in our region of Nigeria, accounting for much morbidity and mortality. Herein we report the outcome of neonates with ABE seen at our centre.

Methodology: We established a surveillance of children who had ABE and returned to follow-up from prospective cases of ABE (2012-2014). ABE was diagnosed based on a bilirubin-induced neurologic dysfunction score of ≥ 1. Kernicterus was subsequently established based on a history of developmental delays, hearing impairments and abnormal physical and neurologic examinations at follow-up age ≥3 months.

Result: Five hundred fifty-one neonates had hyperbilirubinaemia of whom 104 (18.8%) had ABE. Mean transcutaneous bilirubin using the Ingram icterometer was 18.3 mg/dl ± SD 1.9 [(12.5-19.1), total serum bilirubin of 18.1 ± 10.9] (range: 10.3-64 mg/dl). Sixty-five infants returned for follow-up (41 males and 24 females); mean age 9 months (22 days to 17 months). Most (58 of 65; 89.2%) had abnormal neurological findings and 15 (25.9%) had probable kernicterus.

Conclusion: There is a critical need for a National Kernicterus Registry to document all cases of kernicterus and formulate an effective treatment and prevention policy.

MeSH terms

  • Bilirubin / blood*
  • Child
  • Developmental Disabilities / epidemiology
  • Developmental Disabilities / physiopathology*
  • Female
  • Follow-Up Studies
  • Humans
  • Hyperbilirubinemia / epidemiology
  • Infant
  • Infant, Newborn
  • Jaundice, Neonatal / diagnosis*
  • Jaundice, Neonatal / epidemiology
  • Kernicterus / diagnosis*
  • Kernicterus / epidemiology
  • Male
  • Morbidity
  • Mortality
  • Neurologic Examination
  • Nigeria / epidemiology
  • Prevalence
  • Prospective Studies

Substances

  • Bilirubin