A Rare Adult Case with Diffuse Segmental Membranous Glomerulonephritis

Intern Med. 2017;56(13):1691-1695. doi: 10.2169/internalmedicine.56.8298. Epub 2017 Jul 1.

Abstract

A 71-year-old man with hypertension and diabetes mellitus presented with proteinuria. Laboratory data showed proteinuria of 3.1 g/g creatinine, serum albumin of 3.5 g/dL and serum creatinine of 1.03 mg/dL without autoantibodies. A renal biopsy revealed segmental granular IgG depositions on glomerular capillary walls. Electron microscopy showed segmentally subepithelial, intramembranous and mesangial deposits. Diffuse segmental membranous glomerulonephritis (MGN) was diagnosed with only IgG1 deposition and without M-type phospholipase A2 receptor or thrombospondin type-1 domain-containing 7A staining, suggesting secondary MGN with an unknown target antigen in immune deposits. Physicians should keep in mind the existence of segmental MGN to better understand the clinicopathological characteristics.

Keywords: IgG subclass; adult; membranous glomerulonephritis; renal pathology; secondary membranous glomerulonephritis.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Glomerulonephritis, Membranous / diagnosis*
  • Glomerulonephritis, Membranous / immunology*
  • Humans
  • Immunoglobulin G / immunology
  • Kidney Glomerulus / pathology
  • Male
  • Microscopy, Electron
  • Proteinuria / pathology
  • Receptors, Phospholipase A2 / immunology

Substances

  • Immunoglobulin G
  • PLA2R1 protein, human
  • Receptors, Phospholipase A2