Liver disease predicts mortality in patients with X-linked immunodeficiency with hyper-IgM but can be prevented by early hematopoietic stem cell transplantation

J Allergy Clin Immunol. 2018 Jan;141(1):405-408.e7. doi: 10.1016/j.jaci.2017.06.036. Epub 2017 Jul 26.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Biomarkers
  • Biopsy
  • Diagnostic Imaging
  • Hematopoietic Stem Cell Transplantation* / methods
  • Humans
  • Hyper-IgM Immunodeficiency Syndrome, Type 1 / complications*
  • Hyper-IgM Immunodeficiency Syndrome, Type 1 / diagnosis
  • Hyper-IgM Immunodeficiency Syndrome, Type 1 / mortality*
  • Hyper-IgM Immunodeficiency Syndrome, Type 1 / prevention & control*
  • Kaplan-Meier Estimate
  • Liver Diseases / complications*
  • Liver Diseases / diagnosis
  • Time-to-Treatment

Substances

  • Biomarkers