Lipodystrophic laminopathy: Lamin A mutation relaxes chromatin architecture to impair adipogenesis

J Cell Biol. 2017 Sep 4;216(9):2607-2610. doi: 10.1083/jcb.201707090. Epub 2017 Aug 15.

Abstract

The familial partial Dunnigan lipodystrophy, characterized by subcutaneous fat loss, is frequently caused by an R482W mutation in lamin A. In this issue, Oldenburg et al. (2017. J. Cell Biol. https://doi.org/10.1083/jcb.201701043) demonstrate that this mutation impairs the ability of lamin A to repress the anti-adipogenic miR-335, providing a potential molecular mechanism for the disease.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adipogenesis
  • Chromatin*
  • Lamin Type A / genetics*
  • Lipodystrophy, Familial Partial / genetics
  • Mutation

Substances

  • Chromatin
  • Lamin Type A